Publications by authors named "Robin Ziegler"

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Increasing Enzyme Mannose-6-Phosphate Levels but Not Miglustat Coadministration Enhances the Efficacy of Enzyme Replacement Therapy in Pompe Mice.
Allyson Anding, Sofia Kinton, Kaitlyn Baranowski, Alexander Brezzani, Hilde De Busser, Robin Ziegler

J Pharmacol Exp Ther· November 2023

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Secreted acid sphingomyelinase as a potential gene therapy for limb girdle muscular dystrophy 2B.
Daniel C Bittel, Sen Chandra Sreetama, Goutam Chandra, Robin Ziegler, Kanneboyina Nagaraju

J Clin Invest· January 2022

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Priapism in a Fabry disease mouse model is associated with upregulated penile nNOS and eNOS expression.
Xing-Li Meng, Erland Arning, Mary Wight-Carter, Taniqua S Day, Siamak Jabbarzadeh-Tabrizi, Robin J Ziegler

J Inherit Metab Dis· March 2018

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Reversibility of neuropathology in Tay-Sachs-related diseases.
María-Begoña Cachón-González, Susan Z Wang, Robin Ziegler, Seng H Cheng, Timothy M Cox

Hum Mol Genet· February 2014

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Gene transfer corrects acute GM2 gangliosidosis--potential therapeutic contribution of perivascular enzyme flow.
M Begoña Cachón-González, Susan Z Wang, Rosamund McNair, Josephine Bradley, David Lunn, Robin Ziegler

Mol Ther· August 2012

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Systemic administration of AAV8-α-galactosidase A induces humoral tolerance in nonhuman primates despite low hepatic expression.
Jennifer B Nietupski, Gregory D Hurlbut, Robin J Ziegler, Qiuming Chu, Bradley L Hodges

Mol Ther· November 2011

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Adeno-associated virus-mediated expression of β-hexosaminidase prevents neuronal loss in the Sandhoff mouse brain.
Timothy J Sargeant, Susan Wang, Josephine Bradley, Nicolas J C Smith, Animesh A Raha, Robin J Ziegler

Hum Mol Genet· November 2011

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Distribution of acid sphingomyelinase in rodent and non-human primate brain after intracerebroventricular infusion.
Robin J Ziegler, Ernesto A Salegio, James C Dodge, John Bringas, Christopher M Treleaven

Exp Neurol· October 2011

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Adeno-associated virus-mediated expression of acid sphingomyelinase decreases atherosclerotic lesion formation in apolipoprotein E(-/-) mice.
Andrew J Leger, Leocadia M Mosquea, Lingyun Li, Weilien Chuang, Joshua Pacheco, Robin Ziegler

J Gene Med· June 2011

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Preexisting immunity and low expression in primates highlight translational challenges for liver-directed AAV8-mediated gene therapy.
Gregory D Hurlbut, Robin J Ziegler, Jennifer B Nietupski, Joseph W Foley, Lisa A Woodworth

Mol Ther· November 2010

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Evaluation of systemic follistatin as an adjuvant to stimulate muscle repair and improve motor function in Pompe mice.
Joseph W Foley, Scott D Bercury, Patrick Finn, Seng H Cheng, Ronald K Scheule, Robin J Ziegler

Mol Ther· September 2010

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Glycoengineered acid alpha-glucosidase with improved efficacy at correcting the metabolic aberrations and motor function deficits in a mouse model of Pompe disease.
Yunxiang Zhu, Ji-Lei Jiang, Nathan K Gumlaw, Jinhua Zhang, Scott D Bercury, Robin J Ziegler

Mol Ther· June 2009

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Pulmonary delivery of recombinant acid sphingomyelinase improves clearance of lysosomal sphingomyelin from the lungs of a murine model of Niemann-Pick disease.
Robin J Ziegler, Claire Brown, Christine M Barbon, Anne Marie D'Angona, Edward H Schuchman

Mol Genet Metab· May 2009

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Systemic Insulin-like growth factor-1 reverses hypoalgesia and improves mobility in a mouse model of diabetic peripheral neuropathy.
Qiuming Chu, Rod Moreland, Nelson S Yew, Joseph Foley, Robin Ziegler

Mol Ther· August 2008

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Ability of adeno-associated virus serotype 8-mediated hepatic expression of acid alpha-glucosidase to correct the biochemical and motor function deficits of presymptomatic and symptomatic Pompe mice.
Robin J Ziegler, Scott D Bercury, Jonathan Fidler, Michael A Zhao, Joseph Foley

Hum Gene Ther· June 2008

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Combination brain and systemic injections of AAV provide maximal functional and survival benefits in the Niemann-Pick mouse.
Marco A Passini, Jie Bu, Jonathan A Fidler, Robin J Ziegler, Joseph W Foley

Proc Natl Acad Sci U S A· May 2007

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Correction of the biochemical and functional deficits in fabry mice following AAV8-mediated hepatic expression of alpha-galactosidase A.
Robin J Ziegler, Maribeth Cherry, Christine M Barbon, Chester Li, Scott D Bercury

Mol Ther· March 2007

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Correction of the Biochemical and Functional Deficits in Fabry Mice Following AAV8-mediated Hepatic Expression of α-galactosidase A.
Robin J Ziegler, Maribeth Cherry, Christine M Barbon, Chester Li, Scott D Bercury

Mol Ther· March 2007

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Effective gene therapy in an authentic model of Tay-Sachs-related diseases.
M Begoña Cachón-González, Susan Z Wang, Andrew Lynch, Robin Ziegler, Seng H Cheng

Proc Natl Acad Sci U S A· July 2006

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AAV8-mediated hepatic expression of acid sphingomyelinase corrects the metabolic defect in the visceral organs of a mouse model of Niemann-Pick disease.
Christine M Barbon, Robin J Ziegler, Chester Li, Donna Armentano, Maribeth Cherry

Mol Ther· September 2005

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AAV2 vector harboring a liver-restricted promoter facilitates sustained expression of therapeutic levels of alpha-galactosidase A and the induction of immune tolerance in Fabry mice.
Robin J Ziegler, Scott M Lonning, Donna Armentano, Chester Li, David W Souza

Mol Ther· February 2004

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Partial correction of the alpha-galactosidase A deficiency and reduction of glycolipid storage in Fabry mice using synthetic vectors.
Malgorzata Przybylska, I-Huan Wu, Hongmei Zhao, Robin J Ziegler, Jennifer D Tousignant

J Gene Med· January 2004

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Demonstration of feasibility of in vivo gene therapy for Gaucher disease using a chemically induced mouse model.
John Marshall, Kerry Anne McEachern, Julie A Cavanagh Kyros, Jennifer B Nietupski, Tracey Budzinski, Robin J Ziegler

Mol Ther· August 2002

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Adenovirus-transduced lung as a portal for delivering alpha-galactosidase A into systemic circulation for Fabry disease.
Chester Li, Robin J Ziegler, Maribeth Cherry, Michael Lukason, Robert J Desnick

Mol Ther· June 2002

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Correction of the nonlinear dose response improves the viability of adenoviral vectors for gene therapy of Fabry disease.
Robin J Ziegler, Chester Li, Maribeth Cherry, Yunxiang Zhu, Donna Hempel

Hum Gene Ther· May 2002

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